| Name : | Branched chain fatty acid beta-oxidation |
| Description : | Branched chain fatty acids have a carbon scaffold with methyl branches. The enzymes that allow the properly beta-oxidation are:
a) ACOX2 (it belongs to the acyl-CoA oxidases family and carries on the first dehydrogenation), ACOX3 (it belongs to the acyl-CoA oxidases family and is involved in branched chain FA oxidation only in rodentia. It carries on the first dehydrogenation), c) HSD17B4 (D-PBE) (hydration and dehydrogenation again, rely on the bifunctional protein), d) SCPX (Sterol carrier protein X carries on the thyolitic cleavage). |
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