YEAR |
FIRST AUTHOR |
JOURNAL |
TITLE |
2009 |
Bao Lige |
Mol. Biol. Cell |
Role of an ancestral d-bifunctional protein containing two sterol-carrier protein-2 domains in lipid uptake and trafficking in Toxoplasma.[Pubmed] |
2007 |
Justyna Paprocka |
|
Clinical and neuropathological picture of familial encephalopathy with bifunctional protein deficiency.[Pubmed] |
2006 |
Tam Nguyen |
J. Cell. Sci. |
Failure of microtubule-mediated peroxisome division and trafficking in disorders with reduced peroxisome abundance.[Pubmed] |
2005 |
I Soorani-Lunsing |
J. Inherit. Metab. Dis. |
Normal very-long-chain fatty acids in peroxisomal D-bifunctional protein deficiency: a diagnostic pitfall.[Pubmed] |
2005 |
Shan Zha |
Prostate |
Peroxisomal branched chain fatty acid beta-oxidation pathway is upregulated in prostate cancer.[Pubmed] |
2004 |
V Schröder |
Acta Neuropathol. |
Optico-cochleo-dentate degeneration associated with severe peripheral neuropathy and caused by peroxisomal D-bifunctional protein deficiency.[Pubmed] |
2004 |
Johan Edqvist |
J. Biol. Chem. |
Plants express a lipid transfer protein with high similarity to mammalian sterol carrier protein-2.[Pubmed] |
2004 |
Sacha Ferdinandusse |
J. Lipid Res. |
Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of long-chain dicarboxylic acids.[Pubmed] |
2003 |
Jolein Gloerich |
J. Lipid Res. |
A novel HPLC-based method to diagnose peroxisomal D-bifunctional protein enoyl-CoA hydratase deficiency.[Pubmed] |
2003 |
Sacha Ferdinandusse |
Mol. Genet. Metab. |
Evidence for increased oxidative stress in peroxisomal D-bifunctional protein deficiency.[Pubmed] |
2003 |
Cristiano Rizzo |
Pediatr. Res. |
Characteristic acylcarnitine profiles in inherited defects of peroxisome biogenesis: a novel tool for screening diagnosis using tandem mass spectrometry.[Pubmed] |
2003 |
Satomi Matsuoka |
Eukaryotic Cell |
MFE1, a member of the peroxisomal hydroxyacyl coenzyme A dehydrogenase family, affects fatty acid metabolism necessary for morphogenesis in Dictyostelium spp.[Pubmed] |
2002 |
Sacha Ferdinandusse |
Biochem. Biophys. Res. Commun. |
Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of leukotrienes.[Pubmed] |
2002 |
S Ferdinandusse |
Am. J. Hum. Genet. |
Reinvestigation of peroxisomal 3-ketoacyl-CoA thiolase deficiency: identification of the true defect at the level of d-bifunctional protein.[Pubmed] |
2002 |
Paton Paton |
Prenat. Diagn. |
Molecular analysis of genomic DNA allows rapid, and accurate, prenatal diagnosis of peroxisomal D-bifunctional protein deficiency.[Pubmed] |
2001 |
S Ferdinandusse |
J. Lipid Res. |
Identification of the peroxisomal beta-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid.[Pubmed] |
2001 |
Su Su |
J. Biol. Chem. |
Peroxisomal straight-chain Acyl-CoA oxidase and D-bifunctional protein are essential for the retroconversion step in docosahexaenoic acid synthesis.[Pubmed] |
2001 |
Clayton Clayton |
Biochem. Soc. Trans. |
Clinical consequences of defects in peroxisomal beta-oxidation.[Pubmed] |
2000 |
M Itoh |
Brain Res. |
Developmental and pathological expression of peroxisomal enzymes: their relationship of D-bifunctional protein deficiency and Zellweger syndrome.[Pubmed] |
2000 |
S Ferdinandusse |
J. Lipid Res. |
Peroxisomal fatty acid oxidation disorders and 58 kDa sterol carrier protein X (SCPx). Activity measurements in liver and fibroblasts using a newly developed method.[Pubmed] |
2000 |
M Baes |
J. Biol. Chem. |
Inactivation of the peroxisomal multifunctional protein-2 in mice impedes the degradation of not only 2-methyl-branched fatty acids and bile acid intermediates but also of very long chain fatty acids.[Pubmed] |
2000 |
T Hashimoto |
Cell Biochem. Biophys. |
Peroxisomal beta-oxidation enzymes.[Pubmed] |
1999 |
N Shimozawa |
Biochem. Biophys. Res. Commun. |
Functional heterogeneity of C-terminal peroxisome targeting signal 1 in PEX5-defective patients.[Pubmed] |
1999 |
P Mooijer |
Hum. Mol. Genet. |
Enoyl-CoA hydratase deficiency: identification of a new type of D-bifunctional protein deficiency.[Pubmed] |
1998 |
P Vreken |
J. Lipid Res. |
Sensitive analysis of serum 3alpha, 7alpha, 12alpha,24-tetrahydroxy- 5beta-cholestan-26-oic acid diastereomers using gas chromatography-mass spectrometry and its application in peroxisomal D-bifunctional protein deficiency.[Pubmed] |
1998 |
E Ijlst |
Proc. Natl. Acad. Sci. U.S.A. |
Peroxisomal D-hydroxyacyl-CoA dehydrogenase deficiency: resolution of the enzyme defect and its molecular basis in bifunctional protein deficiency.[Pubmed] |
1997 |
T Jiang |
J. Biochem. |
Physiological role of D-3-hydroxyacyl-CoA dehydratase/D-3-hydroxyacyl-CoA dehydrogenase bifunctional protein.[Pubmed] |
1990 |
Baker Baker |
FASEB J. |
A common ancestor for Candida tropicalis and dehydrogenases that synthesize antibiotics and steroids.[Pubmed] |